Most patients diagnosed with clear cell chondrosarcoma were in 3rd and 4th decades of life. Most common location is in epiphysis. The most common sites of involvement are the proximal femur, proximal humerus, distal femur and proximal tibia.
The most common symptoms are pain and swelling, that usually are of long duration. There may be limitation of the range of motion of the involved joint.
On radiographs, these tumors are well-circumscribed mixed lucent and sclerotic lesions with an active appearance.
Treatment and prognosis: En bloc resection with a wide margin of normal bone and soft tissue is the procedure of choice.